Silverstone - Best's Disease, Hereditary Retinal Dystrophy, RG, AF, ICG
Best's disease, is a hereditary retinal dystrophy involving the retinal pigment epithelium (RPE), and leads to a characteristic bilateral yellow egg-yolk Birdshot chorioretinopathy is a rare form of bilateral posterior uveitis affecting the eye. It causes severe, progressive inflammation of both the choroid and retina. Affected individuals are almost exclusively caucasian and usually diagnosed in the fourth to sixth decade of their lives.appearance of the macula. This disease tends to present itself in childhood or early adulthood and usually portends a good visual prognosis.